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Evidence profile

SGA QEM trio rare disease screening

Canonical evidence interpretation profile for trio-based whole-genome sequencing in rare Mendelian disease screening.

Technical information

Profile UID
sga_qem_trio_rare_disease_v1
Version
1.0
Visibility
Community
Domain
Clinical Genetics
Standard
SGA-QEM-1.0 v1.0
Maintainer
Swiss Genomics Association
Status
canonical
Scope
Trio-based whole-genome sequencing for rare Mendelian disease screening
Source file
evidence_interpretation_rules_e7af8e5dc03accac17b690d244995afa.html
Checksum
e7af8e5dc03accac17b690d244995afa

How to read this table

Rule name, meaning, and flag describe how available data are interpreted before QuantBayes is run.

Each rule can return TRUE, FALSE, or NA. Under this QEM convention, only FALSE contributes supporting evidence.

Evidence shows the human interpretation. Matrix shows the binary value sent to QuantBayes.

Rules

Evidence interpretation rules

5 rules
Rule nameMeaningFlagEvidenceMatrix
Parent genotype unavailable
parent_gt_unavailable
Parental genetic data are missing, so inheritance cannot be assessed. This contributes 0.TRUENo0
Parent genotype unavailable
parent_gt_unavailable
Parental genetic data are available and inheritance can be evaluated. This contributes 1.FALSEYes1
Parent genotype unavailable
parent_gt_unavailable
It is unknown whether parental genetic data are available. This contributes 0.NANo0
Parent genotype mechanistically inconsistent AR
parent_gt_mechanistically_inconsistent_ar
Parental results rule out an autosomal recessive explanation. This contributes 0.TRUENo0
Parent genotype mechanistically inconsistent AR
parent_gt_mechanistically_inconsistent_ar
Parental results are compatible with autosomal recessive inheritance. This contributes 1.FALSEYes1
Parent genotype mechanistically inconsistent AR
parent_gt_mechanistically_inconsistent_ar
Parental genetic data are missing, so inheritance cannot be checked. This contributes 0.NANo0
Compound heterozygous phase inconsistent
compound_het_phase_inconsistent
The two variants are arranged in a way that cannot explain disease together. This contributes 0.TRUENo0
Compound heterozygous phase inconsistent
compound_het_phase_inconsistent
The two variants are arranged in a way that could explain disease together. This contributes 1.FALSEYes1
Compound heterozygous phase inconsistent
compound_het_phase_inconsistent
Information on how the variants are arranged is unavailable. This contributes 0.NANo0
De novo mechanism not excluded
denovo_mechanism_not_excluded
Family data rule out the variant being a new genetic change. This contributes 0.TRUENo0
De novo mechanism not excluded
denovo_mechanism_not_excluded
Family data allow the variant to be a new genetic change. This contributes 1.FALSEYes1
De novo mechanism not excluded
denovo_mechanism_not_excluded
Parental genetic data are missing, so this cannot be assessed. This contributes 0.NANo0
Unaffected relative homozygous ALT
unaffected_relative_homozygous_alt
An unaffected family member carries the same genetic change. This contributes 0.TRUENo0
Unaffected relative homozygous ALT
unaffected_relative_homozygous_alt
No unaffected family member is known to carry the same change. This contributes 1.FALSEYes1
Unaffected relative homozygous ALT
unaffected_relative_homozygous_alt
Family health or genetic information is insufficient to assess this. This contributes 0.NANo0